- Benign myoclonus of early infancy is characterized by episodes of myoclonic spasms involving flexion of the trunk, neck, and extremities in a manner resembling the infantile spasms of West syndrome. The spasms typically occur in clusters, only seen in waking state with no change in consciousness during the spells.
- Onset common between 3- 9 months of age and cease within 2 weeks to 8 months.
- Differentials include: West syndrome, myoclonic epilepsy syndromes, shuddering attacks
- An EEG is usually necessary to exclude epilepsy syndromes of infancy which is essentially normal. The developmental and neurologic outcomes are normal
- Treatment is not needed and movements are self-limited
Read classification of ” Paroxysmal Non Epileptic Events PNEE“